Definition and Characteristics of Gigantiform Cementoma
- Rare, autosomal dental tumor
- Benign, but can cause severe disfigurement of the jaw without intervention
- Cause of the tumor is currently unknown
- Exceedingly rare with only a handful of documented cases worldwide
- Cases of Novemthree Siahaan and Ayun Lee highlight the impact and possible heritability of the tumor
Previous Misuse of the Term Gigantiform Cementoma
- Term previously used to describe florid cemento-osseous dysplasia
- Now reserved for an autosomal dominant condition affecting the maxillae
- Primarily affects Caucasian individuals under the age of 10
- Treatment is difficult and requires surgical removal of affected bone
- Reconstruction is necessary after surgical intervention
References
- OMIM Entry -% 137575 - GIGANTIFORM CEMENTOMA, FAMILIAL
- Retrieved from omim.org on 14 June 2019
External Links
- Classification of Gigantiform Cementoma
- OMIM: 137575
- MeSH: C563017
- Wikipedia article on Gigantiform Cementoma (dentistry stub)
- Retrieved from https://en.wikipedia.org/w/index.php?title=Gigantiform_cementoma&oldid=1000967232
Categories and Hidden Categories
- Categories: Dentistry stubs, Rare cancers
- Hidden categories: Articles with short description, Short description is different from Wikidata, All stub articles
Gigantiform cementoma is a rare, autosomal dental tumor. It is benign, but without intervention it can result in severe disfigurement of the jaw. The cause of this tumor is currently unknown. This is an exceedingly rare tumor with only a handful of documented cases worldwide. The most famous case is of Novemthree Siahaan (who died on September 15, 2005), a young Indonesian boy from Batam Island who received medical care in Haulien, Taiwan through a Buddhist missionary from the Tzu Chi Foundation, which was documented on the Discovery Health Channel. Another famous case is a young Korean girl named Ayun Lee (August 26, 2003~) and her father Young-hak Lee whose case has shown that the tumor can be heritable. She is currently under treatment, which she may need to continue until her growth stops in her early 20s.
| Gigantiform cementoma | |
|---|---|
| Specialty | Dentistry |
The term has been used in the past to describe florid cemento-osseous dysplasia, but it is now reserved for an autosomal dominant condition affecting the maxillae. It affects mostly Caucasian people under the age of 10. Treatment is difficult. Surgical removal of the affected bone is needed, and has to be followed by reconstruction.
